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Case Report
Long-term survival in a pediatric patient with a left atrial sarcoma
1 MD, Division of Cardiovascular Surgery, Hospital Metropolitano, Quito, Ecuador
2 MD, PGY 2 Surgery Resident, P.U.C.E.-Hospital Metropolitano, Quito, Ecuador
3 MD, Division of General Surgery, Hospital IESS Quito Sur, Quito, Ecuador
4 MD, Division of Pathology, Hospital Metropolitano, Quito, Ecuador
5 MD, Division of Pediatric Oncology, Hospital Metropolitano, Quito, Ecuador
Address correspondence to:
Santiago A Endara
MD, Edif. Diagnostico 2000, Tercer piso, Av. Mariana de Jesus Oe 7/47 y Conclina, Quito,
Ecuador
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Article ID: 100018C04SE2020
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How to cite this article
Endara SA, Davalos GA, Zavala AB, Molina GA, Mancero JO, Eguiguren JM. Long-term survival in a pediatric patient with a left atrial sarcoma. Edorium J Cardiothorac Vasc Surg 2020;7:100018C04SE2020ABSTRACT
Introduction: Primary cardiac sarcomas are rare (20% of all primary cardiac tumors) and usually lethal (mean survival range from 9.6 to 16.5 months). Undifferentiated sarcomas account for one-third of all cardiac sarcomas incorporate in their malignant mass fibrous and pleomorphic cells. Symptoms will depend on the chambers and the cardiac structures involved. Treatment is based on complete surgical excision when possible, followed by radiotherapy and chemotherapy.
Case Report: We present the case of an 11-year-old boy who was transferred to our hospital after suffering a stroke secondary to embolization from a cardiac tumor located in the left atrium. He underwent surgical resection. Pathology showed a primary cardiac tumor consistent with an undifferentiated pleomorphic sarcoma (UPS). The patient was treated with chemotherapy after the diagnosis was confirmed with immunohistochemistry. He is now 8-years off therapy and asymptomatic.
Conclusion: Primary cardiac tumors are rare. Depending on the exact location, they can present with various symptoms, such as left- or right-sided heart failure, embolic phenomena, or heart conduction abnormalities. Due to its rarity, their diagnosis is usually late; which leads to poor prognosis. High clinical awareness and prompt treatment are essential in these rare diseases.
Keywords: Cancer, Pediatric, Pleomorphic sarcoma, Sarcoma, Tumors of the heart
SUPPORTING INFORMATION
Author Contributions
Santiago A Endara - Substantial contributions to conception and design, Acquisition of data, Analysis of data, Interpretation of data, Drafting the article, Revising it critically for important intellectual content, Final approval of the version to be published
Gerardo A Davalos - Substantial contributions to conception and design, Drafting the article, Final approval of the version to be published
Aldo B Zavala - Substantial contributions to conception and design, Drafting the article, Final approval of the version to be published
Gabriel A Molina - Substantial contributions to conception and design, Acquisition of data, Analysis of data, Interpretation of data, Drafting the article, Revising it critically for important intellectual content, Final approval of the version to be published
José O Mancero - Substantial contributions to conception and design, Drafting the article, Revising it critically for important intellectual content, Final approval of the version to be published
José M Eguiguren - Drafting the article, Revising it critically for important intellectual content, Final approval of the version to be published
Guaranter of SubmissionThe corresponding author is the guarantor of submission.
Source of SupportNone
Consent StatementWritten informed consent was obtained from the patient for publication of this article.
Data AvailabilityAll relevant data are within the paper and its Supporting Information files.
Conflict of InterestAuthors declare no conflict of interest.
Copyright© 2020 Santiago A Endara et al. This article is distributed under the terms of Creative Commons Attribution License which permits unrestricted use, distribution and reproduction in any medium provided the original author(s) and original publisher are properly credited. Please see the copyright policy on the journal website for more information.
